皮肤型结节性多动脉炎
Published in Chinese Journal of Dermatology • Apr 15, 2012
Authors:
顾有守
Abstract
经典的结节性多动脉炎(polyarteritis nodosa,PAN)系1866年由Kussmaul和Maier首先报道的一种致死性血管炎,当时称为结节性动脉周围炎(periarteritis nodosa),1903年Ferrafi将其改称为结节性多动脉炎.Lindberg于1931年首先认识PAN可主要局限于皮肤,称为皮肤型结节性多动脉炎(cutaneous polyarteritis nodosa,CPAN,又称为局限性结节性多动脉炎).CPAN虽主要影响皮肤,但也可有皮肤外的表现,包括发热、疲劳、肌痛、关节痛和周围神经病变.CPAN与PAN皮肤表现相同,但后者有多种器官受累,尤其是肾...
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